M35.0A ICD-10-CM Code: Sjögren syndrome with glomerular disease
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Inpatient Payment Groups (MS-DRG)
MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0, Appendix B.
- MS-DRG 545 — CONNECTIVE TISSUE DISORDERS WITH MCC (MDC 08)
- MS-DRG 546 — CONNECTIVE TISSUE DISORDERS WITH CC (MDC 08)
- MS-DRG 547 — CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC (MDC 08)
A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.
Official Registry Overview & Definition
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for M35.0A in the official ICD-10-CM tabular list.
Includes
Conditions the official ICD-10-CM tabular list includes under this code.
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Excludes1 — Not Coded Here
Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).
- dry mouth, unspecified (R68.2) Compare M35.0A vs R68.2 →
- reactive perforating collagenosis (L87.1) Compare M35.0A vs L87.1 →
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Use Additional Code
Supplementary codes the tabular list directs you to add.
- Use additional code to identify associated manifestations
Change history
- FY2022 — 2021-10-01Added to the code setSjogren syndrome with glomerular diseaseFY2022 changes
Verify Before Coding
- Billable — reportable as written.
From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim.
Contextual Map
Every relationship of M35.0A in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.
Hierarchy
- M35.0 — Sjögren syndrome [Hierarchy]
Referenced by Excludes1 notes
- K11.8 — Other diseases of salivary glands [Excludes1](via M35.0.-): “Sjögren syndrome (M35.0-)”
- R68.2 — Dry mouth, unspecified [Excludes1](via M35.0.-): “dry mouth due to Sjögren syndrome (M35.0-)”
Referenced by Code Also instructions
- I27.21 — Secondary pulmonary arterial hypertension [Code Also](via M35.0.-): “Sjögren syndrome (M35.0-)”
Clinical classification (CCSR)
- MUS024 — Systemic lupus erythematosus and connective tissue disorders [CCSR]
- GEN001 — Nephritis; nephrosis; renal sclerosis [CCSR]
Potential MS-DRG
- DRG 545 — CONNECTIVE TISSUE DISORDERS WITH MCC [MS-DRG]: “CONNECTIVE TISSUE DISORDERS WITH MCC (MDC 08)”
- DRG 546 — CONNECTIVE TISSUE DISORDERS WITH CC [MS-DRG]: “CONNECTIVE TISSUE DISORDERS WITH CC (MDC 08)”
- DRG 547 — CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC [MS-DRG]: “CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC (MDC 08)”
Index entries
- Syndrome, Sjögren, with, gl… — Syndrome, Sjögren, with, glomerular disease [Index term]
Nearest codes (25)
- M35 — Other systemic involvement of connective tissue [Sibling]
- M35.0 — Sjögren syndrome [Sibling]
- M35.00 — Sjögren syndrome, unspecified [Sibling]
- M35.01 — Sjögren syndrome with keratoconjunctivitis [Sibling]
- M35.02 — Sjögren syndrome with lung involvement [Sibling]
- M35.03 — Sjögren syndrome with myopathy [Sibling]
- M35.04 — Sjögren syndrome with tubulo-interstitial nephropathy [Sibling]
- M35.05 — Sjögren syndrome with inflammatory arthritis [Sibling]
- and 17 more
Change history
- FY2022 — Added to the code set [Change history]
Referenced by Other Codes
Clinical classification (AHRQ CCSR):MUS024 — Systemic lupus erythematosus and connective tissue disorders (default); GEN001 — Nephritis; nephrosis; renal sclerosis.
Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.
Potential MS-DRG Relationships (FY2026)
Not on the CMS CC/MCC list — as a secondary diagnosis this code does not change MS-DRG severity.
Named in the grouper logic of 3 MS-DRGs: DRG 545 (MDC 08), DRG 546 (MDC 08), DRG 547 (MDC 08).
From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.
Official ICD-10-CM tabular notes on other codes that name M35.0A or its code family.
2 Excludes1 notes across 2 chapters: K11.8 (via M35.0.-), R68.2 (via M35.0.-).
1 Code Also instructions: I27.21 (via M35.0.-).
Nearest Codes in This Family
Official ICD-10-CM classifications closest to M35.0A in its code family, with their registry titles.
- M35.05 — Sjögren syndrome with inflammatory arthritis
- M35.06 — Sjögren syndrome with peripheral nervous system involvement
- M35.07 — Sjögren syndrome with central nervous system involvement
- M35.08 — Sjögren syndrome with gastrointestinal involvement
- M35.09 — Sjögren syndrome with other organ involvement
- M35.0B — Sjögren syndrome with vasculitis
- M35.0C — Sjögren syndrome with dental involvement
- M35.1 — Other overlap syndromes
- M35.2 — Behçet's disease
- M35.3 — Polymyalgia rheumatica
Indexed Clinical Terms (1)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Syndrome, Sjögren, with, glomerular disease