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ICD-10/E83.110

E83.110 ICD-10-CM Code: Hereditary hemochromatosis

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Inpatient Payment Groups (MS-DRG)

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0 (FY2026), Appendix B.

  • MS-DRG 642 — INBORN AND OTHER DISORDERS OF METABOLISM (MDC 10)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Code Set: Valid FY2026 and FY2027. FY2026 took effect October 1, 2025.

Official Registry Overview & Definition

Hereditary hemochromatosis is a billable ICD-10-CM diagnosis code (E83.110).

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for E83.110 in the official ICD-10-CM tabular list.

Inclusion Terms

Alternative terms the tabular list files under this code.

  • Bronzed diabetes
  • Pigmentary cirrhosis (of liver)
  • Primary (hereditary) hemochromatosis

Excludes1 — Not Coded Here

Conditions that can never be reported with this code; the two are mutually exclusive.

  • GALD (P78.84)
  • Gestational alloimmune liver disease (P78.84)
  • Neonatal hemochromatosis (P78.84)
  • iron deficiency anemia (D50.-)
  • sideroblastic anemia (D64.0-D64.3)
  • dietary mineral deficiency (E58-E61)
  • parathyroid disorders (E20-E21)
  • vitamin D deficiency (E55.-)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 — Not Included Here

Conditions not covered by this code, but which may be reported alongside it when both are present.

  • Ehlers-Danlos syndromes (Q79.6-)

Nearest Codes in This Family

Official ICD-10-CM classifications closest to E83.110 in its code family, with their registry titles.

  • E83.01 — Wilson's disease
  • E83.09 — Other disorders of copper metabolism
  • E83.1 — Disorders of iron metabolism
  • E83.10 — Disorder of iron metabolism, unspecified
  • E83.11 — Hemochromatosis
  • E83.111 — Hemochromatosis due to repeated red blood cell transfusions
  • E83.118 — Other hemochromatosis
  • E83.119 — Hemochromatosis, unspecified
  • E83.19 — Other disorders of iron metabolism
  • E83.2 — Disorders of zinc metabolism

View all codes in the E83 family

Indexed Clinical Terms (4)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Cirrhosis, cirrhotic (hepatic) (liver), pigmentary
  • Diabetes, diabetic (mellitus) (sugar), bronzed
  • Hemochromatosis, hereditary (primary)
  • Hemochromatosis, primary