E83.110 is the authoritative medical code for Hereditary hemochromatosis. This classification is used in medical billing and clinical recording to specify the clinical criteria for hereditary hemochromatosis (ICD-10-CM E83.110), ensuring healthcare documentation aligns with 2026 federal coding standards.
Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.
Official Registry Overview & Definition
Hereditary hemochromatosis is a billable ICD-10-CM diagnosis code E83.110. Inclusion terms: Bronzed diabetes; Pigmentary cirrhosis (of liver); Primary hereditary hemochromatosis. Excludes1 (not coded here): GALD P78.84; Gestational alloimmune liver disease P78.84; Neonatal hemochromatosis P78.84; iron deficiency anemia D50.-; sideroblastic anemia D64.0-D64.3; dietary mineral deficiency E58-E61; parathyroid disorders E20-E21; vitamin D deficiency E55.-; androgen insensitivity syndrome E34.5-; congenital adrenal hyperplasia E25.0; hemolytic anemias attributable to enzyme disorders D55.-; Marfan syndrome Q87.4-; 5-alpha-reductase deficiency E29.1. Excludes2 (not included here): Ehlers-Danlos syndromes Q79.6-.
Official Tabular Instructional Notes
Sequencing, inclusion, and exclusion notes published for E83.110 in the official ICD-10-CM tabular list.
Inclusion Terms
Alternative terms the tabular list files under this code.
- Bronzed diabetes
- Pigmentary cirrhosis (of liver)
- Primary hereditary hemochromatosis
Excludes1 — Not Coded Here
Conditions that can never be reported with this code; the two are mutually exclusive.
- GALD P78.84
- Gestational alloimmune liver disease P78.84
- Neonatal hemochromatosis P78.84
- iron deficiency anemia D50.-
- sideroblastic anemia D64.0-D64.3
- dietary mineral deficiency E58-E61
- parathyroid disorders E20-E21
- vitamin D deficiency E55.-
- androgen insensitivity syndrome E34.5-
- congenital adrenal hyperplasia E25.0
- hemolytic anemias attributable to enzyme disorders D55.-
- Marfan syndrome Q87.4-
- 5-alpha-reductase deficiency E29.1
Excludes2 — Not Included Here
Conditions not covered by this code, but which may be reported alongside it when both are present.
- Ehlers-Danlos syndromes Q79.6-
Frequently Asked Questions (FAQ) & Clinical Guidance
What can't be coded together with E83.110?
Per Excludes1 instructions, E83.110 must not be reported with: GALD (P78.84); Gestational alloimmune liver disease (P78.84); Neonatal hemochromatosis (P78.84); iron deficiency anemia (D50.-).
Can E83.110 be reported alongside related conditions?
Per Excludes2 instructions, E83.110 and the following may both be reported when both are present: Ehlers-Danlos syndromes (Q79.6-).
What conditions are included under E83.110?
Hereditary hemochromatosis includes: Bronzed diabetes; Pigmentary cirrhosis (of liver); Primary (hereditary) hemochromatosis.
Codes in This Family (39)
Official ICD-10-CM classifications in the same code family as E83.110, with their registry titles.
- E83 — Disorders of mineral metabolism
- E83.0 — Disorders of copper metabolism
- E83.00 — Disorder of copper metabolism, unspecified
- E83.01 — Wilson's disease
- E83.09 — Other disorders of copper metabolism
- E83.1 — Disorders of iron metabolism
- E83.10 — Disorder of iron metabolism, unspecified
- E83.11 — Hemochromatosis
- E83.111 — Hemochromatosis due to repeated red blood cell transfusions
- E83.118 — Other hemochromatosis
- E83.119 — Hemochromatosis, unspecified
- E83.19 — Other disorders of iron metabolism
- E83.2 — Disorders of zinc metabolism
- E83.3 — Disorders of phosphorus metabolism and phosphatases
- E83.30 — Disorder of phosphorus metabolism, unspecified
- E83.31 — Familial hypophosphatemia
- E83.32 — Hereditary vitamin D-dependent rickets (type 1) (type 2)
- E83.39 — Other disorders of phosphorus metabolism
- E83.4 — Disorders of magnesium metabolism
- E83.40 — Disorders of magnesium metabolism, unspecified
- E83.41 — Hypermagnesemia
- E83.42 — Hypomagnesemia
- E83.49 — Other disorders of magnesium metabolism
- E83.5 — Disorders of calcium metabolism
- E83.50 — Unspecified disorder of calcium metabolism
- E83.51 — Hypocalcemia
- E83.52 — Hypercalcemia
- E83.59 — Other disorders of calcium metabolism
- E83.8 — Other disorders of mineral metabolism
- E83.81 — Hungry bone syndrome
- E83.82 — Disorders of pyrophosphate metabolism
- E83.820 — Generalized arterial calcification of infancy with unspecified genetic causality
- E83.821 — ENPP1 deficiency causing generalized arterial calcification of infancy
- E83.822 — ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
- E83.823 — ABCC6 deficiency causing generalized arterial calcification of infancy
- E83.824 — ABCC6 deficiency causing pseudoxanthoma elasticum
- E83.825 — CD73 deficiency causing arterial calcification
- E83.89 — Other disorders of mineral metabolism
- E83.9 — Disorder of mineral metabolism, unspecified
Indexed Clinical Terms (4)
Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.
- Cirrhosis, cirrhotic (hepatic) (liver), pigmentary
- Diabetes, diabetic (mellitus) (sugar), bronzed
- Hemochromatosis, hereditary (primary)
- Hemochromatosis, primary
Related Codes & Numerical Sequence (Crawl Map)
Search engines and indexers are advised to traverse adjacent medical codes in this sub-chapter range to find correlated diagnoses or therapeutic procedures: