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Q87.82 ICD-10-CM Code: Arterial tortuosity syndrome

Billing Status: YES. This is a valid, specific, and billable ICD-10-CM reference.

Inpatient Payment Groups (MS-DRG)

MS-DRGs this diagnosis helps define, as principal or secondary, per the CMS ICD-10-CM/PCS MS-DRG Definitions Manual v43.0, Appendix B.

  • MS-DRG 564 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC (MDC 08)
  • MS-DRG 565 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC (MDC 08)
  • MS-DRG 566 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC (MDC 08)

A diagnosis appearing in a group's logic does not by itself determine the DRG assigned to a stay; the grouper uses the full claim.

Official Registry Overview & Definition

Arterial tortuosity syndrome is a billable ICD-10-CM diagnosis code (Q87.82).

Official Tabular Instructional Notes

Sequencing, inclusion, and exclusion notes published for Q87.82 in the official ICD-10-CM tabular list.

Excludes1 — Not Coded Here

Conditions generally not reported together with this code (Excludes1) -- an error unless the two conditions are documented as unrelated to each other (ICD-10-CM Official Guidelines, Section I.A.12.a).

Use Additional Code

Supplementary codes the tabular list directs you to add.

  • Use additional code(s) to identify all associated manifestations

Indexed Clinical Terms (1)

Clinical term phrases from the official ICD-10-CM Index to Diseases and Injuries that map to this code.

  • Syndrome, arterial tortuosity

Frequently Compared Codes

The official Excludes notes on Q87.82 name these codes. Each comparison page covers when the two can — or must not — be reported together.

Change history

  • FY2017 — 2016-10-01
    Added to the code set
    Arterial tortuosity syndrome
    FY2017 changes

Verify Before Coding

  • CC as a secondary diagnosis (FY2026). Can raise the stay's MS-DRG severity tier.

From the code registry, the Medicare Code Editor, and the MS-DRG Definitions Manual. Check it against a full claim.

Relationships & Classification

Other codes that name Q87.82 or its code family, from the CMS ICD-10-CM tabular instructional notes. Tabular-note edges are stored at the code family level that carries each note.

2 Excludes1 notes: Q87.A, Q89.7 (via Q87.-).

Potential MS-DRG Relationships (FY2026)

CC — Complication or Comorbidity. Reported as a secondary diagnosis, this code raises the stay's MS-DRG severity tier — except when the principal diagnosis is one of 39 clinically related codes on its CMS exclusion list.

Named in the grouper logic of 3 MS-DRGs: DRG 564 (MDC 08), DRG 565 (MDC 08), DRG 566 (MDC 08).

From the CMS MS-DRG Definitions Manual (Appendices B and C). Actual DRG assignment depends on the complete claim.

Clinical classification (AHRQ CCSR):MAL010 — Other specified and unspecified congenital anomalies (default).

Clinical Classifications Software Refined (CCSR) for ICD-10-CM Diagnoses. Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality.

Related Codes

Same clinical process (MS-DRG)

Acts as CC — raises the severity of other admissions. CMS groups these diagnoses into one MS-DRG principal-diagnosis exclusion process — a CC/MCC on this list never raises severity when the principal diagnosis is also on it.

Q87.19 — Other congenital malformation syndromes predominantly associated with short stature, Q87.2 — Congenital malformation syndromes predominantly involving limbs, Q87.3 — Congenital malformation syndromes involving early overgrowth, Q87.40 — Marfan syndrome, unspecified, Q87.410 — Marfan syndrome with aortic dilation, Q87.418 — Marfan syndrome with other cardiovascular manifestations, Q87.42 — Marfan syndrome with ocular manifestations, Q87.43 — Marfan syndrome with skeletal manifestation, Q87.5 — Other congenital malformation syndromes with other skeletal changes, Q87.81 — Alport syndrome, Q87.83 — Bardet-Biedl syndrome, Q87.84 — Laurence-Moon syndrome, Q87.85 — MED13L syndrome, Q87.86 — Kleefstra syndrome, Q87.87 — Hao-Fountain Syndrome, Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified, Q89.7 — Multiple congenital malformations, not elsewhere classified, Q89.81 — Kabuki syndrome, Q89.89 — Other specified congenital malformations, Q89.9 — Congenital malformation, unspecified, +158 more

Same clinical category (CCSR)

AHRQ's Clinical Classifications Software groups these diagnoses under the same clinical category (Other specified and unspecified congenital anomalies).

Q87.19 — Other congenital malformation syndromes predominantly associated with short stature, Q87.2 — Congenital malformation syndromes predominantly involving limbs, Q87.3 — Congenital malformation syndromes involving early overgrowth, Q87.40 — Marfan syndrome, unspecified, Q87.410 — Marfan syndrome with aortic dilation, Q87.418 — Marfan syndrome with other cardiovascular manifestations, Q87.42 — Marfan syndrome with ocular manifestations, Q87.43 — Marfan syndrome with skeletal manifestation, Q87.5 — Other congenital malformation syndromes with other skeletal changes, Q87.81 — Alport syndrome, Q87.83 — Bardet-Biedl syndrome, Q87.84 — Laurence-Moon syndrome, Q87.85 — MED13L syndrome, Q87.87 — Hao-Fountain Syndrome, Q87.88 — CTNNB1 syndrome, Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified, Q89.01 — Asplenia (congenital), Q89.09 — Congenital malformations of spleen, Q89.1 — Congenital malformations of adrenal gland, Q89.2 — Congenital malformations of other endocrine glands, +59 more

Contextual Map

Every relationship of Q87.82 in one view: hierarchy, official tabular instructions in both directions, clinical classification, risk adjustment, MS-DRG participation, index terms and change history — each edge carrying the CMS source it derives from.

Hierarchy

  • Q00-Q99 — Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (Q00-Q99) (Q00-Q99) [Hierarchy]

Referenced by Excludes1 notes

  • Q87.A — Loeys-Dietz syndrome [Excludes1]: “arterial tortuosity syndrome (Q87.82)” · check together
  • Q89.7 — Multiple congenital malformations, not elsewhere classified [Excludes1](via Q87.-): “congenital malformation syndromes affecting multiple systems (Q87.-)” · check together

Clinical classification (CCSR)

  • MAL010 — Other specified and unspecified congenital anomalies [CCSR]

Potential MS-DRG

  • CC — Complication or Comorbidity [MS-DRG severity]: “As a secondary diagnosis this code can raise the stay's MS-DRG severity tier (CC).”
  • DRG 564 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC [MS-DRG]: “OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC (MDC 08)”
  • DRG 565 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC [MS-DRG]: “OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC (MDC 08)”
  • DRG 566 — OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC [MS-DRG]: “OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC (MDC 08)”

MDC crossing · procedures (18508)

  • MDC 08 — Diseases and Disorders of the Musculoskeletal System and Connective Tissue [MDC crossing]: “Diseases and Disorders of the Musculoskeletal System and Connective Tissue — the grouper's crossing between diagnoses and procedures: a principal diagnosis sets the MDC, and same-MDC procedures move the stay to its surgical DRGs.”
  • 005T0ZZ — Destruction of Spinal Meninges, Open Approach [Same-MDC procedure]: “Destruction of Spinal Meninges, Open Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005T3ZZ — Destruction of Spinal Meninges, Percutaneous Approach [Same-MDC procedure]: “Destruction of Spinal Meninges, Percutaneous Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005T4ZZ — Destruction of Spinal Meninges, Percutaneous Endoscopic Approach [Same-MDC procedure]: “Destruction of Spinal Meninges, Percutaneous Endoscopic Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005W0Z3 — Destruction of Cervical Spinal Cord using Laser Interstitial Thermal Therapy, Open Approach [Same-MDC procedure]: “Destruction of Cervical Spinal Cord using Laser Interstitial Thermal Therapy, Open Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • 005W0ZZ — Destruction of Cervical Spinal Cord, Open Approach [Same-MDC procedure]: “Destruction of Cervical Spinal Cord, Open Approach — grouped in MDC 08, the procedure side of this code's crossing.” · check together
  • and 18503 more

Index entries

  • Syndrome, arterial tortuosity[Index term]

Nearest codes (25)

  • Q87 — Other specified congenital malformation syndromes affecting multiple systems [Sibling]
  • Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance [Sibling]
  • Q87.1 — Congenital malformation syndromes predominantly associated with short stature [Sibling]
  • Q87.11 — Prader-Willi syndrome [Sibling]
  • Q87.19 — Other congenital malformation syndromes predominantly associated with short stature [Sibling]
  • Q87.2 — Congenital malformation syndromes predominantly involving limbs [Sibling]
  • Q87.3 — Congenital malformation syndromes involving early overgrowth [Sibling]
  • Q87.4 — Marfan syndrome [Sibling]
  • and 17 more

Change history

  • FY2017 — Added to the code set [Change history]

Nearest Codes in This Family

Official ICD-10-CM classifications closest to Q87.82 in its code family, with their registry titles.

  • Q87.42 — Marfan syndrome with ocular manifestations
  • Q87.43 — Marfan syndrome with skeletal manifestation
  • Q87.5 — Other congenital malformation syndromes with other skeletal changes
  • Q87.8 — Other specified congenital malformation syndromes, not elsewhere classified
  • Q87.81 — Alport syndrome
  • Q87.83 — Bardet-Biedl syndrome
  • Q87.84 — Laurence-Moon syndrome
  • Q87.85 — MED13L syndrome
  • Q87.86 — Kleefstra syndrome
  • Q87.87 — Hao-Fountain Syndrome

View all codes in the Q87 family